Kasabach- Meritt Syndrome- A Rare Cause of Bleeding In a Neonate
نویسنده
چکیده
Kasabach-Merritt Syndrome (KMS) is a rare disorder that can affect infants from the time of birth or later in infancy. Diagnosis of KMS is made based on the constellation of hemangioma, thrombocytopenia, and coagulopathy. Our case presented at birth with hemangioma on perineal area and bleeding tendancy. On evaluation thrombocytopenia and coaguloepathy were found and diagnosis KMS was established supported by histopathology. Baby was treated with oral predinisolone and showed complete resolution of hemangioma and normalization of lab parameters.
منابع مشابه
Anesthestic management of Kassabach-Meritt Phenomenon in an adult: case report
BACKGROUND Kasabach-Merritt phenomenon (KMP) is characterized by a vascular tumor with profound thrombocytopenia and consumptive coagulopathy that may presents significant challenges for anesthesiologist. CASE PRESENTATION An 87-year-old man presented with kaposiform hemangioendothelioma involving the right leg in critical condition due to massive bleeding. Hematology investigations indicated...
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